Lamellar Ichthyosis Market Insight and Market Forecast

Lamellar Ichthyosis (LI) is a type of autosomal recessive congenital Ichthyosis (ARCI), which is a clinically and genetically heterogeneous group of dermatological scaly skin disorders.

Infants affected with LI are born encased in a hyperkeratotic translucent membrane, known as collodion baby, and within 2 weeks develop large, thick, brownish lamellar scales with minimal erythema. Additionally, LI is associated with crumpled ears, alopecia, eclabium, and ectropion.

Total Prevalence of Inherited Ichthyosis in France was estimated at 13.3 per million people and the prevalence of lamellar Ichthyosis was 4.5 per million people.

In a study conducted in Japan with 220 patients treated for ARCI and Ichthyosis syndromes, 95 patients were observed with Nonbullous Congenital Ichthyosiform erythroderma, 30 with lamellar Ichthyosis, and 15 with harlequin Ichthyosis (Kurosawa et al.)

A study conducted in Spain on 144 patients with ARCI has shown that among these patients, 62.5% had classic Lamellar Ichthyosis and 30.6% had congenital Ichthyosiform Erythroderma (Martín et al).

The Age-standardized Prevalent cases of Lamellar Ichthyosis (LI) recorded in the United States is proportionally decent.

The lowest prevalence population of Lamellar Ichthyosis (LI) was recorded in Japan (in 7MM).

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